Case History: Two-year-old female born from nonconsanguineous marriage presented with cough with expectoration and high-grade fever for six days.
Two-year-old female born from nonconsanguineous marriage presented with cough with expectoration and high-grade fever for six days.
Figure 1. Plain chest radiograph in postero-anterior view of a two-year-old female with complaints of cough with expectoration and high grade fever for six days.
Figure 2. Right inferior pulmonary veins form a common trunk and drain into supra-diaphragmatic IVC instead of its normal drainage into left atrium (arrow).
Figure 3. Right inferior pulmonary veins form a single trunk (arrow).
Figure 4. Right superior pulmonary vein drains into left atrium along with all pulmonary veins on the left side draining into the same chamber (arrow).
Figure 5. Right common inferior pulmonary veins draining into supra-diaphragmatic inferior vena cava (arrow).
Diagnosis: Congenital pulmonary venolobar syndrome, also known as scimitar syndrome
Right lung appears hypoplastic.
Scimitar syndrome, or pulmonary venolobar syndrome, is a rare congenital anomaly, characterized by anomalous venous return from the right lung (to the systemic venous drainage, rather than directly to the left atrium).
The syndrome can be associated with congenital heart disease.
